Hyperimmunoglobulin E syndrome in two siblings
Hyperimmunoglobulin E recurrent infection syndrome (HIES) is characterized by recurrent skin and lung infections, eczema, elevated serum immunoglobulin E (IgE) levels (>2000 IU/mL), various connective tissue, skeletal, and vascular abnormalities.1 We describe herein two brothers with HIES and documented the complications and management of such involvement.
hyper-IgE syndrome, atopic dermatitis, primary immunodeficiency, infection.
Submitted: 2011-07-20 00:32:19
Published: 2011-11-28 14:00:56
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