Giant virilizing adrenocortical carcinoma in a girl presenting with mutism
- Huseyin Demirbilek
Diyarbakir Children Diseases Hospital, Pediatric Endocrinology, Diyarbakir, Turkey. firstname.lastname@example.org
- Serhan Kupeli
Diyarbakir Children Diseases Hospital, Pediatric Oncology, Diyarbakir, Turkey.
- Mehmet Nuri Ozbek
Diyarbakir Children Diseases Hospital, Pediatric Endocrinology, Diyarbakir, Turkey.
- Ahmet Baran
Diyarbakir Children Diseases Hospital,Radiology, Diyarbakir, .
- Murat Kemal Cigdem
Dicle University, Pediatric Surgery, Diyarbakir, Turkey.
- Selver Ozekinci
Dicle University, Pathology, Diyarbakir, Turkey.
Adrenocortical tumors (ACT) are rare tumors of childhood. There are some difficulties in classification of pediatric ACT as adenoma or carcinoma. Prognostic characteristics as well as treatment choices are controversial. In general virilizing ACT are presenting at earlier age than non-functional tumors. Here we presented an early presented, delayed diagnosed giant virilizing adrenocortical tumor in a girl presented with mutism. Present case is interesting both in complaints at the presentation and the nature of tumor biology. Based on previously reported prognostic criteria present case had borderline characteristics and treatment option was only total resection of the tumor without adjuvant chemotherapy.